Pelvic hemangiopericytoma: A case report and review of the literature

Abstract

Extrauterine pelvic hemangiopericytomas are rare tumors with malignant potential. Herein, we report a case of a 55-year-old male who presented with hydronephrosis and obstructive urinary symptoms. Cystoscopy, imaging and biopsy were unable to provide a definitive preoperative diagnosis. He underwent pelvic mass resection, and final pathology revealed malignant hemangiopericytoma. The patient is being closely monitored with serial imaging, and remains disease-free at 23 months of post-operative follow-up without adjuvant therapy. Our experience and evidence from the existing literature suggests that given the rarity of these tumors, adherence to standard oncologic principles is necessary to ensure adequate resection and appropriate follow-up.

Keywords: Case report; Hemangiopericytoma; Malignant solitary fibrous tumor; Surgical resection.

Fig. 1

Excretory phase computed tomography showed (A) a centrally necrotic pelvic mass displacing a contrast-filled urinary bladder to the right and (B) resulting in severe left hydroureteronephrosis with cortical thinning. (C) Coronal and (D) sagittal views on magnetic resonance imaging confirmed presence of a pelvic mass anterior to the rectum and displacing the urinary bladder.

Fig. 2

(A) Grossly, the 10.5 cm pelvic mass appeared well-circumscribed with a smooth surface. (B) Sectioning revealed a fleshy mass with a central necrotic lesion.