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Case Reports
. 2020 Jul-Aug;95(4):484-489.
doi: 10.1016/j.abd.2019.09.030. Epub 2020 May 5.

Annular epidermolytic ichthyosis: a case report and literature review

Emanuella Stella Mikilita  1 , Irina Paipilla Hernandez  1 , Ana Letícia Boff  1 , Ana Elisa Kiszewski  2
Affiliations
Case Reports

Annular epidermolytic ichthyosis: a case report and literature review

Emanuella Stella Mikilita et al. An Bras Dermatol. 2020 Jul-Aug.

Abstract

Annular epidermolytic ichthyosis is a rare subtype of epidermolytic ichthyosis that is characterized by erythematous, polycyclic, and migratory scaly plaques accompanied by palmoplantar keratoderma. This report presents the case of an 8-year-old girl who developed migratory, erythematous, scaly plaques associated with palmoplantar keratoderma. The initial hypothesis was erythrokeratodermia variabilis et progressiva; however, the finding of epidermolytic hyperkeratosis in histopathological examination led to the diagnosis of annular epidermolytic ichthyosis.

Keywords: Hyperkeratosis, epidermolyitic; Ichthyosiform erythroderma; Ichthyosis.

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Figures

Figure 1
Figure 1
Hyperkeratosis in palms.
Figure 2
Figure 2
Erythematous, hyperkeratotic plaque, with prominent and geographical border in the cervical region. Yellowish keratotic plaques at the angle of the mouth and chin.
Figure 3
Figure 3
(A) Erythematous, keratotic plaques with prominent and geographical borders on the arms, forearms, cervical, armpits, lateral region of the trunk, and umbilical and supra-umbilical regions. (B) The same patient a month later, presenting erythematous and hyperkeratotic plaques along the entire arm, forearm, and anterior chest, sparing the umbilical and supra-umbilical regions.
Figure 4
Figure 4
Acanthosis, papillomatosis, and hyperkeratosis with epidermolysis of the granular layer (Hematoxylin & eosin, ×400).
See this image and copyright information in PMC

References

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