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Review
. 2018 Jan 15;9(1):2996-3005.
doi: 10.19102/icrm.2018.090103. eCollection 2018 Jan.

The Use of Implantable Cardioverter-defibrillators in the Prevention of Sudden Cardiac Death: A Focus on Congenital Heart Disease and Inherited Arrhythmia Syndromes

Sarah A Goldstein  1 , Cary C Ward  1   2 , Sana M Al-Khatib  1   2
Affiliations
Review

The Use of Implantable Cardioverter-defibrillators in the Prevention of Sudden Cardiac Death: A Focus on Congenital Heart Disease and Inherited Arrhythmia Syndromes

Sarah A Goldstein et al. J Innov Card Rhythm Manag. .

Abstract

Some congenital heart diseases (CHDs) and inherited arrhythmia syndromes are associated with an increased risk of sudden cardiac death (SCD). Appropriate selection criteria for implantable cardioverter-defibrillator (ICD) implantation in these patients are poorly defined due to a paucity of data available from randomized clinical trials, leading to current guidelines relying more on non-randomized studies and expert opinions to make their recommendations. This review describes available evidence-based risk stratification methods for identifying patients at risk for SCD, as well as current guideline-driven management strategies for the use of ICDs in patients with CHD and inherited arrhythmia syndromes.

Keywords: Congenital heart disease; implantable cardioverter-defibrillator; inherited arrhythmia syndrome; sudden cardiac death; ventricular arrhythmia.

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Conflict of interest statement

The authors report no conflicts of interest for the published content.

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