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Case Reports
. 2020 Jun 1;35(3):399-401.
doi: 10.21470/1678-9741-2018-0414.

Primary Biatrial Cardiac Rhabdomyosarcoma

Tetsuro Uchida  1 , Yoshinori Kuroda  1 , Mitsuaki Sadahiro  1
Affiliations
Case Reports

Primary Biatrial Cardiac Rhabdomyosarcoma

Tetsuro Uchida et al. Braz J Cardiovasc Surg. .

Abstract

Primary malignant neoplasms of the heart are rare. Cardiac rhabdomyosarcoma is the second most common primary sarcoma. We report a rare case of a 49-year-old woman with a huge biatrial cardiac rhabdomyosarcoma treated by performing surgical resection followed by salvage chemotherapy for local recurrence. Cardiac sarcoma that occupy both atria are extremely rare. Although the prognosis of cardiac rhabdomyosarcoma is dismal, surgical resection should be recommended as a first line therapy to clarify the diagnosis and to relieve symptoms associated with the tumor.

Keywords: Female; Heart Atria; Heart Neoplasms; Middle Aged; Prognosis; Rhabdomyosarcoma; Sarcoma.

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Conflict of interest statement

No conflict of interest.

Figures

Fig. 1
Fig. 1
A) Echocardiography showed a well demarcated huge mass in the left atrium (arrows); B) Left atrial tumor herniated to the mitral valve orifice; LV=left ventricle; MV=mitral valve; LA=left atrium
Fig. 2
Fig. 2
A) Right atrial tumor originated from the interatrial septum; B) The right atrial tumor was hard, smooth surfaced and white, measuring 20 x 10 mm; C) Left atrial tumor occupying the entire left atrial cavity. D) The left atrial tumor consisted of two globular encapsulated components measuring 105 x 63 mm and 41 x 30 mm respectively. Ao=ascending aorta; T=tumor; IAS=interatrial septum
See this image and copyright information in PMC

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