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Case Reports
. 2020 Jun 24:2020:6810237.
doi: 10.1155/2020/6810237. eCollection 2020.

Rasmussen's Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review

Hedia Klaa  1   2 , Thouraya Ben Younes  1   2 , Hanene Benrhouma  1   2 , Sonia Nagi  2   3 , Aida Rouissi  1   2 , Ichraf Kraoua  1   2 , Ilhem Ben Youssef-Turki  1   2
Affiliations
Case Reports

Rasmussen's Encephalitis: A Report of a Tunisian Pediatric Case and Literature Review

Hedia Klaa et al. Case Rep Neurol Med. .

Abstract

Rasmussen's encephalitis (RE) is a rare progressive inflammatory disease of the central nervous system. It is characterized by unilateral hemispheric atrophy, pharmacoresistant focal seizures, and progressive neurological deficit. The exact etiopathogenesis still remains unknown. Brain imaging plays an important role in diagnosis and follow-up. Fluctuation of lesions in brain imaging was reported in few cases. Herein, we report an additional pediatric case of Rasmussen encephalitis with fluctuating changes in brain MRI.

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Conflict of interest statement

The authors declare that there are no conflicts of interest regarding the publication of this article.

Figures

Figure 1
Figure 1
EEG showing asymmetric background activity with the left frontotemporal intercritical discharges.
Figure 2
Figure 2
Serial MRIs in T2 and FLAIR sequences showing hyperintensity in the left frontoinsular region, lenticular, and caudate nuclei (a). Seven months after the first MRI, persistence of hyperintensity, left fronto-insular cortical and homolateral striatum atrophy, and dilatation of the ipsilateral ventricular system (b). After 3 years and 9 months from the first MRI, we noticed an increase of the left hemispheric atrophy (c).
See this image and copyright information in PMC

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