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Case Reports
. 2020 Jul 3;12(7):e8980.
doi: 10.7759/cureus.8980.

Secundum Atrial Septal Defect With Early Presentation of Eisenmenger Syndrome and Right-Heart Failure: A Rare Case Report and Literature Review

Jahanzeb Malik  1 , Umar Ikram  1 , Ahmed Kamal  1 , Ahsan Khalid Sr  1 , Tayyaba Zahid  1
Affiliations
Case Reports

Secundum Atrial Septal Defect With Early Presentation of Eisenmenger Syndrome and Right-Heart Failure: A Rare Case Report and Literature Review

Jahanzeb Malik et al. Cureus. .

Abstract

Eisenmenger syndrome, the most advanced form of pulmonary arterial hypertension (PAH), poses a considerable risk to the survival and quality of life of patients. It is more commonly seen in large intra-cardiac defects like ventricular septal defects (VSD) or patent ductus arteriosus (PDA), and rarely in atrial septal defects (ASD). Early diagnosis is the single most important step in the definitive management of the condition; otherwise, only conservative treatment can be offered. In this report, we present the case of a 20-year-old female patient diagnosed with Eisenmenger syndrome secondary to a large secundum ASD. The patient responded well to medical treatment.

Keywords: atrial septal defect; congenital heart disease; eisenmenger; right heart cath; right heart failure; right to left shunt.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. ECG showing right bundle branch block
ECG: electrocardiogram
Figure 2
Figure 2. Large secundum atrial septal defect with a dilated right heart (black arrow)
See this image and copyright information in PMC

References

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