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. 2020 Sep;34(9):1900-1913.
doi: 10.1111/jdv.16752. Epub 2020 Aug 24.

Updated S2K guidelines on the management of pemphigus vulgaris and foliaceus initiated by the european academy of dermatology and venereology (EADV)

P Joly  1 , B Horvath  2 , Α Patsatsi  3 , S Uzun  4 , R Bech  5 , S Beissert  6 , R Bergman  7 , P Bernard  8 , L Borradori  9 , M Caproni  10 , F Caux  11 , G Cianchini  12 , M Daneshpazhooh  13 , D De  14 , M Dmochowski  15 , K Drenovska  16 , J Ehrchen  17 , C Feliciani  18 , M Goebeler  19 , R Groves  20 , C Guenther  21 , S Hofmann  22 , D Ioannides  23 , C Kowalewski  24 , R Ludwig  21 , Y L Lim  25 , B Marinovic  26 , A V Marzano  27   28 , J M Mascaró Jr  29 , D Mimouni  30 , D F Murrell  31 , C Pincelli  32 , C P Squarcioni  11 , M Sárdy  33 , J Setterfield  34 , E Sprecher  35   36 , S Vassileva  16 , K Wozniak  37 , S Yayli  38 , G Zambruno  39 , D Zillikens  40 , M Hertl  41 , E Schmidt  40
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Free article

Updated S2K guidelines on the management of pemphigus vulgaris and foliaceus initiated by the european academy of dermatology and venereology (EADV)

P Joly et al. J Eur Acad Dermatol Venereol. 2020 Sep.
Free article

Abstract

Background: Pemphigus encompasses a group of life-threatening autoimmune bullous diseases characterized by blisters and erosions of the mucous membranes and skin. Before the era of immunosuppressive treatment, pemphigus was almost always fatal. Due to its rarity, only few randomized controlled therapeutic trials are available. Recently, rituximab has been approved as first-line treatment for moderate and severe pemphigus vulgaris in Europe and the United States.

Objectives: The Autoimmune blistering diseases Task Force of the European Academy of Dermatology and Venereology (EADV) has initiated a throughout update of the guideline for the management of patients with pemphigus.

Results: The guidelines for the management of pemphigus were updated, and the degree of consent among all task force members was included. The final version of the guideline was consented by the European Dermatology Forum (EDF) and several patient organizations.

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References

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