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Review
. 2020 Sep 28;13(9):e235786.
doi: 10.1136/bcr-2020-235786.

Adult-onset Still's disease with concurrent thrombotic thrombocytopenic purpura: case report and literature review

Ryohei Kato  1 , Tomoyuki Ikeuchi  2 , Katsuyuki Tomita  2 , Akira Yamasaki  3
Affiliations
Review

Adult-onset Still's disease with concurrent thrombotic thrombocytopenic purpura: case report and literature review

Ryohei Kato et al. BMJ Case Rep. .

Abstract

Thrombotic thrombocytopenic purpura (TTP) is rare complication resulting from adult-onset Still's disease (AOSD). We report the case of a 69-year-old Japanese man who initially presented with fever and joint pain and was diagnosed as having concurrent AOSD with TTP 1 month later. He had extremely high ferritin levels (32 696 ng/mL). He initially responded to plasma exchange but subsequently died of septic shock. AOSD accompanied by extremely high ferritin levels might be considered a sign of concurrent TTP.

Keywords: rheumatology; thrombotic thrombocytopenic purpura.

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Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
A peripheral blood film with May-Giemsa stain showed schistocytes and dacrocytes.
See this image and copyright information in PMC

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