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Case Reports
. 2020 May;36(3):234-236.
doi: 10.1007/s12055-019-00896-x. Epub 2020 Jan 8.

Double outlet right ventricle, pulmonary stenosis and congenital mitral stenosis

Lincoln Samuel  1 , George Varghese Kurien  2 , Joel Devasia Vazhakatt  3 , Sajan Koshy  1
Affiliations
Case Reports

Double outlet right ventricle, pulmonary stenosis and congenital mitral stenosis

Lincoln Samuel et al. Indian J Thorac Cardiovasc Surg. 2020 May.

Abstract

A 4-year-old girl child was diagnosed with double outlet right ventricle (DORV), severe pulmonary stenosis, and supramitral ring. This case is presented to bring to light this rare association. Through this report, we aim to stress importance of assessing mitral apparatus on echocardiography during evaluation for situations like DORV and Tetralogy of Fallot (TOF). The physiological differences in such situations as opposed to their isolated counterparts and special postoperative outcomes are also discussed.

Keywords: Parachute mitral valve; Supramitral ring; Tetralogy of Fallot (TOF).

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Conflict of interest statement

Conflict of interestThe authors declare that they have no conflict of interest.

Figures

Fig. 1
Fig. 1
Supramitral ring being excised, forceps points towards partly excised ring.
Fig. 2
Fig. 2
Polar light sign in echocardiogram
See this image and copyright information in PMC

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