Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2020 Sep;11(Suppl 1):73-77.
doi: 10.1007/s13193-020-01070-1. Epub 2020 Apr 25.

Ball in the Wall: Mesenteric Fibromatosis-a Rare Case Report

Affiliations
Case Reports

Ball in the Wall: Mesenteric Fibromatosis-a Rare Case Report

Abhinav Deshpande et al. Indian J Surg Oncol. 2020 Sep.

Abstract

Introduction: Mesenteric fibromatosis-desmoid tumor of mesentery is a rare benign soft tissue tumor of mesentery. On CT, it mimics gastrointestinal stromal tumor (GIST).

Case report: A 44-year-old female with small intestinal mass, preoperatively diagnosed radiologically and pathologically as GIST.

Conclusion: Mesenteric fibromatosis is a rare tumor often mistaken for GIST. Histopathology and immunohistochemistry is the key as management of both the tumors differs.

Keywords: Desmoid tumor of mesentery; GIST; Mesenteric fibromatosis.

PubMed Disclaimer

Figures

Fig. 1
Fig. 1
CT scan image shows a dumbbell-shaped tumor (marked by red arrow) attached to the small intestine
Fig. 2
Fig. 2
CT scan sagittal section image shows a dumbbell-shaped tumor (marked by red arrow) attached to the small intestine
Fig. 3
Fig. 3
Gross of the resected specimen showing a dumbbell-shaped tumor, cut section solid white whirling seen. A smaller tumor marked by red circle is seen separately
Fig. 4
Fig. 4
Microscopy (× 10) shows a spindle-shaped neoplasm arising from serosa. Muscularis propria and subserosa is unremarkable
Fig. 5
Fig. 5
Microscopy (× 40) shows spindle cells arranged in whorls and storiform pattern. Collagenized fibers are also seen. Mitosis is not seen

References

    1. Zhou YL, Boardman LA, Miller RC. Genetic testing for young-onset colorectal cancer: case report and evidence-based clinical guidelines. Radiol Oncol. 2010;44:57–61. - PMC - PubMed
    1. Gurbuz AK, Giardiello FM, Petersen GM, Krush AJ, Offerhaus GJ, Booker SV, Kerr MC, Hamilton SR. Desmoid tumours in familial adenomatous polyposis. Gut. 1994;35:377–381. - PMC - PubMed
    1. Bridge JA, Sreekantaiah C, Mouron B, Neff JR, Sandberg AA, Wolman SR. Clonal chromosomal abnormalities in desmoid tumors. Implications for histopathogenesis. Cancer. 1992;69:430–436. - PubMed
    1. Alman BA, Li C, Pajerski ME, Diaz-Cano S, Wolfe HJ. Increased beta-catenin protein and somatic APC mutations in sporadic aggressive fibromatoses (desmoid tumors) Am J Pathol. 1997;151:329–334. - PMC - PubMed
    1. Smith AJ, Lewis JJ, Merchant NB, Leung DH, Woodruff JM, Brennan MF. Surgical management of intra-abdominal desmoid tumours. Br J Surg. 2000;87:608–613. - PubMed

Publication types

LinkOut - more resources