Conservative treatment of monolateral giant renal angiomyolipoma in a patient with Tuberous Sclerosis Complex (TSC): A case report

Abstract

Tuberous sclerosis complex has several renal manifestations like angiomyolipomas. We report a case of a giant AML and discuss its diagnosis and treatment. A 42-year-old woman was admitted to emergency department due to flank pain and hematuria. The patient had history of mental retardation and epilepsy. Abdominal CT without contrast medium revealed a large mass with a fat/blood content inside. On those findings, we diagnosed the patient a bleeding giant AML. We performed selective embolization of the bleeding source with subsequent conservative management. TSC-associated AMLs occur more frequently as multiple lesions and grow to larger size than idiopathic AML.

Keywords: Conservative treatment; Giant angiomyolipomas; Hematuria; Tuberous sclerosis complex.

Fig. 1

CT abdomen with contrast medium in coronal scan which in arterial phase shows active bleeding within the neoformation (red arrow). (For interpretation of the references to colour in this figure legend, the reader is referred to the Web version of this article.)

Fig. 2

Angiography and selective embolization of the branch of the right renal artery source of bleeding (red arrow). (For interpretation of the references to colour in this figure legend, the reader is referred to the Web version of this article.)