Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2021 Jan;133(1-2):65-72.
doi: 10.1007/s00508-020-01753-3.

Clinical-Pathological Conference Series from the Medical University of Graz : Case No 170: A 33-year-old psychologist with severe dyspnea and right-sided chylothorax

Philipp K Bauer  1 , Martin Flicker  2 , Elisabeth Fabian  3 , Holger Flick  4 , Luka Brcic  5 , Bernadette Liegl-Atzwanger  5 , Michael Janisch  6 , Michael Fuchsjäger  6 , Horst Olschewski  4 , Guenter J Krejs  7
Affiliations

Clinical-Pathological Conference Series from the Medical University of Graz : Case No 170: A 33-year-old psychologist with severe dyspnea and right-sided chylothorax

Philipp K Bauer et al. Wien Klin Wochenschr. 2021 Jan.
No abstract available

Keywords: Cystic lung disease; Lymphangioleiomyomatosis; Sirolimus; VEGF-D.

PubMed Disclaimer

Conflict of interest statement

P.K. Bauer, M. Flicker, E. Fabian, H. Flick, L. Brcic, B. Liegl-Atzwanger, M. Janisch, M. Fuchsjäger, H. Olschewski and G.J. Krejs declare that they have no competing interests.

Figures

Fig. 1
Fig. 1
Chest X‑ray (in expiration) with subtotal opacity of the right lung and merely residual ventilation of the right upper lobe (arrow) as well as a mediastinal shift to the left
Fig. 2
Fig. 2
CT of the chest. Axial (a) and coronal (b) images (soft tissue window setting); massive right pleural effusion (asterisk), atelectasis of the right middle and lower lung lobes (arrowheads) as well as a marked mediastinal shift to the left (arrows). Axial image (c; lung window setting); multiple small lung cysts (diameter up to 6 mm; arrows) as well as extensive ground glass opacities (arrowheads)
Fig. 3
Fig. 3
Histological presentation of the retroperitoneal mass. Spindle tumor cells without marked atypia are present, displaying eosinophilic cytoplasm and interspersed blood vessel structures (hematoxylin-eosin staining, objective ×4 and ×20 inlet)
Fig. 4
Fig. 4
Normal follow-up chest X‑ray a; p.a. and b; lateral) after treatment with sirolimus for 6 months
See this image and copyright information in PMC

References

    1. Light RW. Clinical practice. Pleural effusion. N Engl J Med. 2002;346(25):1971–1977. - PubMed
    1. Doerr CH, Allen MS, Nichols FC, Ryu JH. Etiology of chylothorax in 203 patients. Mayo Clin Proc. 2005;80(7):867–870. - PubMed
    1. Agrawal V, Doelken P, Sahn SA. Pleural fluid analysis in chylous pleural effusion. Chest. 2008;133(6):1436–1441. - PubMed
    1. Maldonado F, Hawkins FJ, Daniels CE, Doerr CH, Decker PA, Ryu JH. Pleural fluid characteristics of chylothorax. Mayo Clin Proc. 2009;84(2):129–133. - PMC - PubMed
    1. Braun SR, Everett ED, Perry MC, Sunderrajan EV. Concise textbook of pulmonary medicine. New York: Elsevier; 1989.

Substances