[Review of Kawasaki disease complicated with macrophage activation syndrome]
- PMID: 33120474
- DOI: 10.3760/cma.j.cn112140-20200407-00354
[Review of Kawasaki disease complicated with macrophage activation syndrome]
Abstract
巨噬细胞活化综合征(Macrophage activation syndrome,MAS)属川崎病(Kawasaki disease,KD)罕见并发症,KD合并MAS(KD-MAS)发病急,病死率高,临床需尽早识别、及时治疗。本文对近年来KD-MAS的流行病学、发病机制、早期识别、诊断及治疗进展进行综述。.
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