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. 2021 Dec;36(6):1110-1113.
doi: 10.1007/s00455-020-10208-w. Epub 2020 Nov 4.

A Rare Syndrome Causing Neurogenic Dysphagia

Antonio Zito #  1 , Paola Bini #  2 , Massimiliano Todisco  3   4 , Giuseppe Cosentino  1   5 , Simone Mauramati  6 , Matteo Paoletti  7 , Vincenzo Marasco  8 , Enrico Marchioni  2 , Enrico Alfonsi  5
Affiliations

A Rare Syndrome Causing Neurogenic Dysphagia

Antonio Zito et al. Dysphagia. 2021 Dec.
No abstract available

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Conflict of interest statement

The authors declare that they have no conflict of interest.

Figures

Fig. 1
Fig. 1
Brain magnetic resonance imaging of the patient. Bilateral hyperintense alterations of the subcortical white matter of the frontal operculum, mostly on the right side, on axial FLAIR (a) and coronal T2-weighted sequences (b). The lesions are hypointense and do not show contrast enhancement on axial T1-weighted sequences (c). The Milky Way sign is evident on both T1- and T2-weighted sequences
Fig. 2
Fig. 2
Electrokinesiographic/electromyographic study of swallowing in our FCMS patient (a) and a representative trace from a healthy subject (b). The first channel records the LPM using a piezoelectric transducer applied to the skin over the cricothyroid membrane (*LPM during the pharyngeal phase). The second channel records breathing activity by means of a nasal cannula connected to a piezoelectric transducer (negative and positive deflections represent inspiration and expiration, respectively) (**swallowing apnea during the pharyngeal phase, while the arrowhead shows the post-swallowing inspiration in the FCMS patient). The third channel records the CPEMG with a percutaneous concentric needle (the arrow indicates the pause of the CPEMG during the pharyngeal phase, physiologically present in the healthy subject and absent in the FCMS patient). The fourth channel records the SHEMG using surface electrodes (***SHEMG triggering an effective swallowing in the healthy subject). The vertical line represents the occurrence of the “white-out” on simultaneously performed FEES (shown on the right panel). CPEMG electromyographic activity of the cricopharyngeal muscle, FCMS Foix–Chavany–Marie syndrome, FEES fiberoptic endoscopic evaluation of swallowing, LPM laryngopharyngeal mechanogram, SHEMG electromyographic activity of the suprahyoid/submental muscles
See this image and copyright information in PMC

References

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