Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2020 Oct 31;2020(10):rjaa418.
doi: 10.1093/jscr/rjaa418. eCollection 2020 Oct.

Lipofibromatous Hamartoma in a Hispanic Patient with macrodactyly: a rare peripheral nerve tumor causing recurrent carpal tunnel syndrome

Marcantonio V Pinci  1 , Gerardo Olivella  1 , Manuel Rodríguez  1 , Hans W Hess-Arcelay  1 , Norman Ramírez  2 , Christian Foy-Parilla  1
Affiliations
Case Reports

Lipofibromatous Hamartoma in a Hispanic Patient with macrodactyly: a rare peripheral nerve tumor causing recurrent carpal tunnel syndrome

Marcantonio V Pinci et al. J Surg Case Rep. .

Abstract

This is a rare case of a 42-year-old Hispanic male with macrodactyly who presented with recurrent carpal tunnel syndrome (CTS) due to Lipofibromatous Hamartoma (LFH). A slowly growing mass in his right palm with pain and numbness, along with motor and sensory deficits in the median nerve distribution, was reported since the past year prior to visit. Previous open carpal tunnel release was performed at 16 years of age due to CTS without complications. The diagnosis of LFH was made based on ultrasound, electromyography test and physical examination. An extended open carpal tunnel release with transection of transverse ligament was performed. The 24-month postoperative evaluation showed complete resolution of symptoms. This report illustrates the management of a recurrent CTS due to LFH in a Hispanic adult patient with macrodactyly that was successfully treated with a carpal tunnel decompression.

PubMed Disclaimer

Figures

Figure 1
Figure 1
Clinical photographs of a Hispanic adult with macrodactyly and Lipofibromatous Hamartoma (red arrow).
Figure 2
Figure 2
Intraoperative photographs of a Hispanic adult with lipofibromatous hamartoma (yellow arrow).
See this image and copyright information in PMC

References

    1. Hoellwarth J, Goitz R. Lipofibromatous Hamartoma of the palmar cutaneous branch of the median nerve. J Hand Microsurg. 2018;10:109–12. - PMC - PubMed
    1. Tahiri Y, Xu L, Kanevsky J, Luc M. Lipofibromatous hamartoma of the median nerve: a comprehensive review and systematic approach to evaluation, diagnosis, and treatment. J Hand Surg Am. 2013;38:2055–67. - PubMed
    1. Louis DS, Hankin FM, Greene TL, Dick HM. Lipofibromas of the median nerve: long-term follow-up of four cases. J Hand Surg Am. 1985;10:403–8. - PubMed
    1. Bains R, Kotwal A, Saeed W. Recurrent carpal tunnel syndrome in a child due to fibrolipomatous hamartoma of the median nerve successfully treated by limited excision and decompression. J Plast Reconstr Aesthet Surg. 2006;59:1394–7. - PubMed
    1. Silverman TA, Enzinger FM. Fibrolipomatous hamartoma of nerve. A clinicopathologic analysis of 26 cases. Am J Surg Pathol. 1985;9:7–14. - PubMed

Publication types