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Case Reports
. 2021 Jan;38(1):233-236.
doi: 10.1111/pde.14425. Epub 2020 Nov 11.

Dermatofibrosarcoma protuberans (DFSP) in children: A combined multidisciplinary approach

Aseel Sleiwah  1 , Cristina Psomadakis  2 , Emma Craythorne  2 , Catherine M Stefanato  3 , William Rickaby  3 , Alistair Robson  4 , Jemima E Mellerio  2 , Aina Greig  1
Affiliations
Case Reports

Dermatofibrosarcoma protuberans (DFSP) in children: A combined multidisciplinary approach

Aseel Sleiwah et al. Pediatr Dermatol. 2021 Jan.

Abstract

Dermatofibrosarcoma protuberans (DFSP) is rare, comprising (1%-6%) of all sarcomas. The incidence is less than one per million before the age of 20. It is a locally aggressive tumor with a low risk of metastasis. We share our experience in the management of three pediatric patients with complex cases of DFSP in a combined surgical approach involving plastic and dermatologic surgery, using the slow Mohs micrographic surgery technique.

Keywords: cutaneous surgery; dermatofibrosarcoma; dermatopathology; neoplasms; skin.

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References

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