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Case Reports
. 2021 May 1;32(3):e290-e292.
doi: 10.1097/SCS.0000000000007205.

Orthognathic Surgery in Cleidocranial Dysplasia

Navid Pourtaheri  1 , Omar Allam  2 , Ludmila Chandler  2 , Derek M Steinbacher  2
Affiliations
Case Reports

Orthognathic Surgery in Cleidocranial Dysplasia

Navid Pourtaheri et al. J Craniofac Surg. .

Abstract

Optimal surgical correction of the craniofacial manifestations of cleidocranial dysplasia (CCD) has not been established due to the rarity of the condition. A 27-year-old female with CCD is presented. She underwent virtual surgical planning (VSP) followed by LeFort-I disimpaction, bone grafting, bilateral sagittal-split osteotomy, genioplasty, submental lipectomy, and targeted facial fat grafting. The patient necessitated 15-mm of vertical maxillary disimpaction centrally, stabilized with wide maxillary plates and interpositional allogenic fibula grafts. Six-month postoperative examination demonstrated improved appearance and functional symptoms. Skeletal relationships were normalized on computed tomography (CT) and there was minimal change between immediate and 6-month postoperative CT measurements, demonstrating a stable result. Orthognathic surgery used to establish dentofacial harmony in patients with CCD can test the extremes of single-stage facial skeletal expansion. Use of VSP, wide maxillary plates, and interpositional bone grafts can help optimize maxillary expansion and stability, while concurrent fat redistribution optimizes facial aesthetics.

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Conflict of interest statement

The authors report no conflicts of interest.

References

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