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Case Reports
. 2020 Jul-Dec;26(2):166-169.
doi: 10.4103/njs.NJS_35_19. Epub 2020 Jul 27.

Desmoid-type Fibromatosis of the Splenic Hilum: A Rare Tumor at an Unusual Location

Ana Sánchez-Gollarte  1 , Fernando Mendoza-Moreno  1 , Marina Pérez-González  1 , Manuel Díez-Alonso  1 , José María Mugüerza-Huguet  1 , María Del Rocío Díez-Gago  2 , Fernando Noguerales-Fraguas  1 , Alberto José Gutiérrez-Calvo  1
Affiliations
Case Reports

Desmoid-type Fibromatosis of the Splenic Hilum: A Rare Tumor at an Unusual Location

Ana Sánchez-Gollarte et al. Niger J Surg. 2020 Jul-Dec.

Abstract

Desmoid-type fibromatoses (DTFs), also known as desmoid tumors, are benign but infiltrative neoplasms that often appear next to previous surgical site. Intra-abdominal tumors usually involve the mesentery, but splenic hilum is an unusual localization. We present a case of a desmoid tumor of the splenic hilum laparoscopically resected in a 70-year-old male with a previous history of chromophobe renal cell carcinoma and ocular spindle melanoma. Although benign, desmoid tumors might be infiltrative and produce serious complications. Treatment remains controversial, ranging from surgery and medical therapies to observation. Management of DTF must be individualized, considering the risk of complications and recurrence.

Keywords: Desmoid tumor; desmoid-type fibromatosis; splenic hilum tumor.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Enhanced computed tomography showing the tumor adjacent to splenic hilum
Figure 2
Figure 2
Macroscopic view of the tumor
Figure 3
Figure 3
Immunohistochemical stain showing nuclear beta-catenin
See this image and copyright information in PMC

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