Congenitally Corrected Transposition of the Great Arteries at Age 88 Years

Abstract

Most patients with congenital heart disease are diagnosed shortly after birth; however, some patients are overlooked and diagnosed in adulthood. We present the case of a man in whom congenitally corrected transposition of the great arteries (CCTGA) was first diagnosed at the age of 88 years. CCTGA is a rare disease; patients without frequently associated cardiac anomalies are considered to have long life expectancies; however, their prognosis remains unclear. This case is the oldest patient at the time of CCTGA diagnosis in the literature, which may provide new insights for CCTGA without frequently associated cardiac anomalies.

Figure 1

An electrocardiogram showed bradycardia of 48 beats per minute due to third-degree atrioventricular block, inversion of all complexes in lead I, marked right axis deviation with 152 degree, reverse R-wave progression in precordial leads, and Q-wave in leads I, aVL, and V6.

Figure 2

(A-F) Chest computed tomography images. The aorta arose from the anatomic right ventricle with the moderator band and the subaortic infundibulum (arrows). The anatomic right ventricle was connected to the left atrium. The right atrium, which was connected to the superior and inferior vena cava, was located on the left side with the presence of situs inversus. (G) A chest radiograph image after transvenous permanent pacemaker implantation. Ao, aorta; IVC, inferior vena cava; LA, left atrium; LV, anatomic left ventricle; PA, pulmonary artery; PV, pulmonary vein; RA, right atrium; RV, anatomic right ventricle; SVC, superior vena cava,.