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Case Reports
. 2020 Oct-Dec;13(4):361-363.
doi: 10.4103/apc.APC_183_20. Epub 2020 Sep 23.

D-transposition of the great arteries with right-sided pulmonary hypoplasia

Mary E Sterrett  1 , Eugene Y Chang  1 , Neha Kumar  2 , Keith B Willan  1 , Sinai C Zyblewski  3
Affiliations
Case Reports

D-transposition of the great arteries with right-sided pulmonary hypoplasia

Mary E Sterrett et al. Ann Pediatr Cardiol. 2020 Oct-Dec.

Abstract

Unilateral pulmonary agenesis or aplasia (UPA) in combination with congenital heart defects is rare and has not been reported in connection with transposition of the great arteries. This case demonstrated dextroposition of the fetal heart, and subsequent scans could not clearly visualize the right pulmonary artery. UPA should be considered in the workup and counseling for a family in the setting of fetal heart malposition, as there is a significant clinical impact.

Keywords: Cardiac malposition; fetal; pulmonary hypoplasia; transposition.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
L Ventricle: Left ventricle, VSD: Ventricular septal defect, R Ventricle: Right ventricle, R Atrium: Right atrium, R Lung: Right lung, AO: Aorta
Figure 2
Figure 2
AO: Aorta, MPA: Main pulmonary artery, LPA: Left pulmonary artery, LSVC: Left superior vena cava
Figure 3
Figure 3
Anterior/posterior X-ray of a neonate. Asymmetric hyperdensity of the right lung, hazy opacification of the right hemithorax, and rightward mediastinal shift
See this image and copyright information in PMC

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