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Case Reports
. 2020 Sep-Oct;25(5):319-322.
doi: 10.4103/jiaps.JIAPS_190_19. Epub 2020 Sep 1.

Congenital Pouch Colon with Segmental Dilatation of Ileum: Congenital Pouch Colon Type 6

Rahul Gupta  1 , Pramila Sharma  1 , Arka Chatterjee  1 , Arvind Kumar Shukla  1 , Arun Kumar Gupta  1 , Lila Dhar Agrawal  1 , Ram Babu Goyal  1
Affiliations
Case Reports

Congenital Pouch Colon with Segmental Dilatation of Ileum: Congenital Pouch Colon Type 6

Rahul Gupta et al. J Indian Assoc Pediatr Surg. 2020 Sep-Oct.

Abstract

Congenital pouch colon (CPC) is classified on the basis of anatomic morphology into five types. Congenital segmental intestinal dilatation associated with anorectal malformation (ARM) is very rare. We are adding two neonates of CPC type 2 associated with segmental dilatation of the ileum to single similar case described in the literature till date. Temporary stomas with excision of either of the pouches should be considered. "Defective mesenchyme formation during organogenesis" due to abnormal mesenchymal precursor cells is hypothesized as the cause for both ARM and different types of CPC.

Keywords: Congenital pouch colon; ileal pouch; type 6.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Intraoperative photographs (a and b) showing cecum (green arrow) with attached appendix (black arrow) opening directly into pouch colon (yellow arrow); segmental dilatation of the terminal ileum (blue arrow) approximately 7–8 cm from ileo-cecal junction is also seen. Diagrammatic representation (c) of case 1 showing double pouch; cecum (green arrow) with attached appendix (blue arrow) opening directly into pouch colon (orange arrow); the pouch is terminating through a fistula into the middle of posterior wall of the bladder (brown arrow). Segmental dilatation of the terminal ileum (black arrow) with proximal normal ileum (white arrow) is appreciated
Figure 2
Figure 2
Intraoperative photograph (a) showing pouch colon (yellow arrow) arising from the cecum (white arrow) with attached appendix (black arrow); segmental dilatation of the terminal ileum (blue arrow) approximately 3–5 cm from ileo-cecal junction is also seen. Intraoperative photograph (b) showing pouch colon (yellow arrow) separated from the fistula; duplicated Mullerian system with right (blue arrow) and left (green arrow) along with both the enlarged and engorged fallopian tubes (chocolate arrow) are seen. A single perineal opening (white arrow) is appreciated. Diagrammatic representation (c) of case 2 showing double pouch; cecum (green arrow) with attached appendix (blue arrow) opening directly into pouch colon (orange arrow); the pouch is terminating into the cloaca (red arrow) through a wide fistula (yellow arrow). Segmental dilatation of the terminal ileum (black arrow) approximately 3–5 cm from ileo-cecal junction with proximal normal ileum (white arrow) is appreciated. Duplicated Mullerian system along with bladder (chocolate arrow) terminating into cloacal chamber (red arrow) is seen
See this image and copyright information in PMC

References

    1. Saxena AK, Mathur P. Classification of congenital pouch colon based on anatomic morphology. Int J Colorectal Dis. 2008;23:635–9. - PubMed
    1. Gupta R. Type 5 congenital pouch colon and its embryopathogenesis. Med J DY PatilVidyapeeth. 2018;11:554–8.
    1. Rai BK, Mirza B, Hashim I, Saleem M. Varied presentation of congenital segmental dilatation of the intestine in neonates: Report of three cases. J Neonatal Surg. 2016;5:55. - PMC - PubMed
    1. Chadha R, Bagga D, Malhotra CJ, Mohta A, Dhar A, Kumar A. The embryology and management of congenital pouch colon associated with anorectal agenesis. J Pediatr Surg. 1994;29:439–46. - PubMed
    1. Mathur P, Prabhu K, Jindal D. Unusual presentations of pouch colon. J Pediatr Surg. 2002;37:1351–3. - PubMed

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