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Case Reports
. 2020 Sep;11(Suppl 2):307-310.
doi: 10.1007/s13193-020-01236-x. Epub 2020 Oct 8.

Bilateral Symmetric Sporadic Osteofibrous Dysplasia: an Unusual Case

Asit Ranjan Mridha  1 , Anubhav Narwal  1 , Adarsh Barwad  1 , Venkatesan Sampat Kumar  1 , Shivanand Gamanagatti  2 , Prashant Ramteke  3
Affiliations
Case Reports

Bilateral Symmetric Sporadic Osteofibrous Dysplasia: an Unusual Case

Asit Ranjan Mridha et al. Indian J Surg Oncol. 2020 Sep.
No abstract available

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Conflict of interest statement

Conflict of InterestThe authors declare that they have no conflict of interest.

Figures

Fig. 1
Fig. 1
A 7-year-old male with osteofibrous dysplasia of bilateral tibia. The AP view radiograph of bilateral legs shows mildly expansile, relatively well-demarcated, longitudinally oriented, confluent, and separate oval-shaped bubbly multiloculated lytic lesions involving diaphysis of the bilateral tibia (arrows) with associated thinning of the anterior cortex and mild tibial bowing. The radiolucent areas are surrounded by sclerotic rim towards the medullary bone
Fig. 2
Fig. 2
A 7-year-old male with osteofibrous dysplasia of bilateral tibia. a Fat-saturated T2-weighted MRI coronal images of bilateral legs show well-defined, mildly expansile, hyperintense multiloculated lesions (arrows) involving diaphysis of the bilateral tibia with associated cortical thinning. b Fat-saturated T2-weighted sagittal images of right leg reveal a well-defined, lobulated, hyperintense lesion involving the diaphysis of right tibia (arrow)
Fig. 3
Fig. 3
A 7-year-old male diagnosed with osteofibrous dysplasia. a and b Haematoxylin and eosin (H&E) stain sections show irregularly arranged woven bone (black arrows) with intervening fibromyxoid collagenous stroma (a, HE, × 40; b, HE, × 200). c Bony trabeculae are rimmed by prominent osteoblasts (white arrows) and the stroma contains bland spindle cells (HE, × 400). d Immunohistochemistry with pan-cytokeratin is negative in tumor cells (× 200)
See this image and copyright information in PMC

References

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