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Case Reports
. 2021 Jan 11;14(1):e236894.
doi: 10.1136/bcr-2020-236894.

Adult-onset Woakes' syndrome: a rare entity

Pedro Salvador  1 , Francisco Moreira da Silva  2 , Rui Fonseca  2
Affiliations
Case Reports

Adult-onset Woakes' syndrome: a rare entity

Pedro Salvador et al. BMJ Case Rep. .

Abstract

Woakes' syndrome (WS) is a rare entity, defined as severe recalcitrant nasal polyposis with consecutive deformity of the nasal pyramid. WS occurs mainly in childhood and its aetiology remains unclear. We report a case of a 68-year old woman, with aspirin-exacerbated respiratory disease, who presented with recurrent nasal polyposis and progressive broadening of the nasal dorsum. CT scan revealed extensive bilateral nasal polyposis and diffuse osteitis, with anterior ethmoidal calcified lesions. The patient underwent revision endoscopic sinus surgery and nasal pyramid deformity was successfully managed without osteotomies.

Keywords: ear; nasal polyps; nose and throat/otolaryngology; otolaryngology / ENT.

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Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
Nasal deformity at presentation.
Figure 2
Figure 2
Obliteration of both nasal cavities by nasal polyps on rigid endoscopy (0°). IT, inferior turbinate; NS, nasal septum.
Figure 3
Figure 3
Coronal CT scan showing bilateral pansinusitis, complete nasal cavities obliteration by soft tissue density polypoid masses, left nasal bone atrophy, diffuse osteitis with bilateral calcified ethmoidal lesions and bulging of the left lamyna paryracea.
Figure 4
Figure 4
Narrowing of the nasal pyramid on follow-up.
See this image and copyright information in PMC

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