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Case Reports
. 2020 Jul-Sep;30(3):162-164.
doi: 10.4103/jcecho.jcecho_36_20. Epub 2020 Nov 9.

Isolated Double-Chambered Right Ventricle - A Rare Entity

Ashok Garg  1 , Deepak Agrawal  2 , G L Sharma  2
Affiliations
Case Reports

Isolated Double-Chambered Right Ventricle - A Rare Entity

Ashok Garg et al. J Cardiovasc Echogr. 2020 Jul-Sep.

Abstract

A double-chambered right ventricle (DCRV) is a rare congenital heart disease and an uncommon cause of congestive heart failure. An anomalous muscle band divides the right ventricle into two cavities: the proximal high-pressure chamber and the distal low-pressure chamber. Most cases are diagnosed and treated during childhood. Furthermore, there is a tendency for progression, if not treated early. Echocardiography is considered useful for the diagnosis of this ailment. Most of the patients have associated congenital anomalies, such as ventricular septal defect, pulmonary stenosis, and subaortic stenosis. Isolated DCRV is a rare entity. Hence, we report a case of an isolated DCRV in an adult patient.

Keywords: Contrast echocardiography; double-chambered right ventricle; echocardiography; pulmonary stenosis; ventricular septal defect.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Electrocardiogram showing increased amplitude of the R wave on V1, inverted T waves on V1–V6, and right-axis deviation suggestive of right ventricular pressure overload
Figure 2
Figure 2
Parasternal long-axis view, arrow indicating marked muscle band protruding from the right ventricular free wall to the interventricular septum
Figure 3
Figure 3
Apical four-chamber view, arrow indicating marked muscle band protruding from the right ventricular free wall to the interventricular septum, dividing the right ventricle into two cavities
Figure 4
Figure 4
Parasternal short-axis view showing turbulent color flow jet with a mosaic pattern through the stenotic mid-right ventricle
Figure 5
Figure 5
Continuous wave Doppler across turbulent jet in the right ventricle showing flow acceleration of 6.0 m/s, corresponding to a pressure gradient of approximately 144 mmHg
Figure 6
Figure 6
Saline contrast echocardiography showing the presence of bubbles only in the right chambers of heart and no communication between either both atria or ventricles
See this image and copyright information in PMC

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