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Case Reports
. 2020 Nov-Dec;65(6):514-515.
doi: 10.4103/ijd.IJD_473_18.

Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association

Iñigo Navarro Fernández  1 , Susana Armesto Alonso  1 , Carlos Duran Vian  1 , L Reguero Del Cura  1 , Carmen González-Vela  2 , Marcos González-López  1
Affiliations
Case Reports

Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association

Iñigo Navarro Fernández et al. Indian J Dermatol. 2020 Nov-Dec.

Abstract

Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease.

Keywords: Linear scleroderma; morphea; primary sclerosing cholangitis.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Atrophic hyperpigmented lesion affecting the patient's dorsal area and posterior proximal upper limb
See this image and copyright information in PMC

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