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Practice Guideline
. 2021 Apr;68(4):e28938.
doi: 10.1002/pbc.28938. Epub 2021 Feb 1.

Surgical management of paratesticular rhabdomyosarcoma: A consensus opinion from the Children's Oncology Group, European paediatric Soft tissue sarcoma Study Group, and the Cooperative Weichteilsarkom Studiengruppe

Timothy N Rogers  1 , Guido Seitz  2 , Jörg Fuchs  3 , Helene Martelli  4 , Roshni Dasgupta  5 , Jonathan C Routh  6 , Douglas S Hawkins  7 , Ewa Koscielniak  8 , Gianni Bisogno  9 , David A Rodeberg  10
Affiliations
Practice Guideline

Surgical management of paratesticular rhabdomyosarcoma: A consensus opinion from the Children's Oncology Group, European paediatric Soft tissue sarcoma Study Group, and the Cooperative Weichteilsarkom Studiengruppe

Timothy N Rogers et al. Pediatr Blood Cancer. 2021 Apr.

Abstract

The treatment of paratesticular rhabdomyosarcoma (PT-RMS) has varied over time and by cooperative group. The International Soft Tissue Sarcoma Database Consortium (INSTRuCT) is a collaboration of the Children's Oncology Group (COG) Soft Tissue Sarcoma Committee, European pediatric Soft tissue sarcoma Study Group (EpSSG), and the Cooperative Weichteilsarkom Studiengruppe (CWS). The INSTRuCT surgical committee has been given charge of the development of internationally applicable consensus guidelines for the surgical treatment of rhabdomyosarcoma. This clinical consensus opinion document addresses accepted principles and areas of controversy, such as scrotal violation and retroperitoneal nodal evaluation, providing an evidence-based guideline for the surgical treatment for PT-RMS.

Keywords: international; paratesticular; pediatric; rhabdomyosarcoma.

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Conflict of interest statement

Author Conflicts of Interest: None

Figures

Figure 1
Figure 1
Borders of the retroperitoneal lymph node sampling area. For right-sided tumors: the right ureter laterally, the anterior aspect of the infra-renal abdominal aorta medially, the anterior aspect of the right common iliac artery all the way to its bifurcation caudally, the renal vessels in the cephalad direction. For left-sided tumor: the left ureter laterally, the medial aspect of the infra-renal inferior vena cava medially, the anterior aspect of the left common iliac artery all the way to its bifurcation caudally, the renal vessels in the cephalad direction
Figure 2
Figure 2
COG review corelating number of retroperitoneal lymph nodes removed versus lymph node positivity
See this image and copyright information in PMC

Comment in

  • Pediatric Urology.
    Canning DA. Canning DA. J Urol. 2022 Apr;207(4):913-915. doi: 10.1097/JU.0000000000002397. Epub 2022 Jan 3. J Urol. 2022. PMID: 34978463 No abstract available.

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