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Case Reports
. 2020 Dec 3;9(2):638-643.
doi: 10.1002/ccr3.3588. eCollection 2021 Feb.

Acquired hemophilia in a 7-year-old girl successfully treated with recombinant FVIIA and steroids: A case report

Gaetano Giuffrida  1 , Uros Markovic  1   2 , Marina Parisi  1 , Daniela Nicolosi  1 , Valeria Calafiore  1
Affiliations
Case Reports

Acquired hemophilia in a 7-year-old girl successfully treated with recombinant FVIIA and steroids: A case report

Gaetano Giuffrida et al. Clin Case Rep. .

Abstract

Acquired hemophilia should be evaluated in pediatric patients with bleeding and isolated prolonged aPTT. Immunosuppressive treatment should be initiated even in minor bleedings. Bypassing agents like rFVIIa can be used in children with success.

Keywords: Acquired hemophilia A; factor VIII deficiency; pediatric population; recombinant factor VII activated.

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Conflict of interest statement

The authors stated that they had no interests that might be perceived as posing a conflict or bias.

Figures

Figure 1
Figure 1
Areas of demarcation showing the left thigh hematoma and the left leg being swollen (arrows)
Figure 2
Figure 2
Magnetic resonance imaging showing notable soft tissue edema/inflammation in the left thigh, hyperintense in T2 and FAT SAT with slight peripheral edema, compatible with a muscular hematoma (arrows)
See this image and copyright information in PMC

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