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Case Reports
. 2021 Jan-Mar;14(1):113-115.
doi: 10.4103/apc.APC_85_20. Epub 2020 Oct 19.

Massive ductal aneurysm in an asymptomatic child with Loeys-Dietz syndrome

Saira Siddiqui  1 , Antonio Polanco  2 , Michael P DiLorenzo  3 , Amee Shah  3 , Michael Snyder  3 , Harry Dietz  4 , Emile Bacha  2 , Kanwal Majeed Farooqi  3
Affiliations
Case Reports

Massive ductal aneurysm in an asymptomatic child with Loeys-Dietz syndrome

Saira Siddiqui et al. Ann Pediatr Cardiol. 2021 Jan-Mar.

Abstract

An asymptomatic 3-year-old with Loeys-Dietz Syndrome (LDS) followed for a small patent ductus arteriosus and dilated aorta was found to have a massive ductal aneurysm on routine surveillance cardiac magnetic resonance. The aneurysm was successfully resected. Serial advanced imaging tools are useful in surveillance, diagnosis, and management in patients with LDS.

Keywords: Cardiac magnetic resonance; Loeys-Dietz syndrome; ductal aneurysm.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
(a) Baseline cardiac MRI at 17 months of age demonstrated dilated AoR and ductal ampulla. (b) Cardiac MRI at 3 years of age demonstrated a large DAA and progressive AoR and AA dilation. (c) Repeat echocardiogram at 3 years of age on the massive DAA on suprasternal arch view. (d) Intraoperatively, the DAA was isolated and resected. (e) An aortic homograft was placed. (f) Postoperative echocardiogram confirmed an unobstructed aortic arch with no residual duct or aneurysm on suprasternal arch view. LPA: Left pulmonary artery, MRI: Magnetic resonance imaging, DAA: Ductal ampulla aneurysm, AoR: Aortic root
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