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Case Reports
. 2021 Mar 30;121(6):555-559.
doi: 10.1515/jom-2020-0284.

The enigmatic fascia: eosinophilic fasciitis

Jonathan A Aun  1   2 , Rachel S Knox  3 , Jared E Roberts  4
Affiliations
Free article
Case Reports

The enigmatic fascia: eosinophilic fasciitis

Jonathan A Aun et al. J Osteopath Med. .
Free article

Abstract

This case report highlights the potentially underrecognized subtype of unilateral eosinophilic fasciitis (EF) in a 28 year old man. With fewer than 300 reported encounters to date, EF is a rare disease that eludes clinicians by presenting as a scleroderma like syndrome. As EF remains a clinical diagnosis, biopsy results may be nonspecific, and the disease can easily be misdiagnosed (or missed entirely) if a full thickness biopsy is not reviewed by a dermatopathologist. The authors also emphasize the importance of internationally accepted diagnostic criteria, of which at least two different sets exist.

Keywords: Shulman syndrome; biopsy; dermatology; dermopathology; diagnosis; eosinophinic fasciitis; scleroderma.

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References

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    1. Johnston, R, Weedon, D. Weedon’s skin pathology essentials, 1st ed. Spain: Elsevier Churchill Livingstone; 2012:239p.

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