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Case Reports
. 2021 Mar 16;16(5):1173-1178.
doi: 10.1016/j.radcr.2021.02.037. eCollection 2021 May.

Prenatal 3D-ultrasound diagnosis of isolated intrahepatic portal-systemic shunt with intact ductus venosus: A case report and literature review

Maxime Van Houdt  1   2 , Johannes van der Merwe  1   2 , Marc Gewillig  3 , Luc De Catte  1   2
Affiliations
Case Reports

Prenatal 3D-ultrasound diagnosis of isolated intrahepatic portal-systemic shunt with intact ductus venosus: A case report and literature review

Maxime Van Houdt et al. Radiol Case Rep. .

Erratum in

Abstract

We present a case of isolated intrahepatic portosystemic shunts with an aorto- hepatic-umbilical connection; prenatally diagnosed with 3D Doppler flow in a 27-year-old patient at 27 weeks of gestation. Fetal karyotyping was normal, detailed evaluation of the venous and cardiovascular system showed a patent ductus venosus and no other abnormalities. These fetuses with isolated intrahepatic shunts are at risk for intra-uterine growth restriction (27%), all cases had a good prognosis with live births. Postnatal follow-up to control shunt closure is vital as persistent shunts may lead to subsequent complications.

Keywords: Intrahepatic portosystemic shunt; Prenatal ultrasound; Umbilical-Portal Venous System.

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Figures

Fig 1
Fig. 1
Twenty-seven-year-old primigravida at 27 weeks of gestation. (A) 3D multiplanar reconstruction & (B) 2D cross sectional sagittal colour doppler ultrasound evaluation of the portosystemic shunts (*). UV, umbilical vein; DV, ductus venosus; SMA, superior mesenteric artery; HA, hepatic artery; SDV, subdiaphragmatic vestibulum; RA, right atrium; Ao, aorta; PV, portal vein.
Fig 2
Fig. 2
(A) 2D-ultrasound image of the dilated umbilical vein in a 27-year old primigravida at 29 weeks of gestation. (B) presence of the small thrombus. (C) postnatal image of the umbilical cord at day 1 in female neonate.
Fig 3
Fig. 3
Six-month-old female patient. (A) Postpartal angiographic image of the portal-hepatic venous shunt (*) in liver segment IV. (B) Angiographic image after coiling. LPV, left portal vein; RAPV, right anterior portal vein; RPPV, right posterior portal vein; RPV, right portal vein.
See this image and copyright information in PMC

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