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Case Reports
. 2021 Jul;36(7):2569-2571.
doi: 10.1111/jocs.15554. Epub 2021 Apr 6.

ACARPA, a rare case of ALCAPA

Thomas Martens  1 , Laurent Demulier  2 , Thierry Bové  1 , Katrien François  1
Affiliations
Case Reports

ACARPA, a rare case of ALCAPA

Thomas Martens et al. J Card Surg. 2021 Jul.

Abstract

An anomalous circumflex coronary artery arising from the right pulmonary artery is very rare. Clinical presentation varies from absence of symptoms to arrhythmia and sudden cardiac death. Since prevalence is very low, no definite therapy has been delineated yet. A 19-year-old patient, previously treated for a vascular ring and mitral valve stenosis, was diagnosed with this anomaly through echocardiography revealing collateral coronary flow, with confirmation of this coronary anomaly on subsequent computed tomography examination. To alleviate the burden for arrhythmia in this young patient, he was successfully treated with surgical reimplantation followed by an uneventful recovery.

Keywords: cardiovascular pathology; congenital heart disease.

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References

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