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Case Reports
. 2021 Apr 10;16(6):1420-1423.
doi: 10.1016/j.radcr.2021.03.023. eCollection 2021 Jun.

Servelle-Martorell syndrome in an adult: A case report with findings on CT angiography

Anh Tuan Tran  1 , Cuong Tran  1 , Nguyen Quyen Le  2 , Thi Huyen Nguyen  1
Affiliations
Case Reports

Servelle-Martorell syndrome in an adult: A case report with findings on CT angiography

Anh Tuan Tran et al. Radiol Case Rep. .

Erratum in

Abstract

Servelle-Martorell syndrome, also known as angio-osteohypotrophic syndrome, is a congenital venous malformation that rarely involves the arterial system. There are many different, mainly conservative, treatment methods. We present the case of a 28-year-old woman with a history of left arm and back lesions, which appeared at birth and had enlarged over time. She had been diagnosed with a vascular malformation but had not yet received treatment. She presented to our hospital with numbness in her left arm and was diagnosed with Servelle-Martorell syndrome based on computed tomography (CT) angiography. This case emphasizes that CT angiography is a useful modality for evaluating the extent of the venous malformations in patients with Servelle-Martorell syndrome.

Keywords: Servelle-Martorell syndrome; Venous malformations.

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Figures

Fig 1
Fig. 1
The left arm and back were large and deformed with bluish tint (red arrows). (Color version of figure is available online.)
Fig 2
Fig. 2
The anechoic, completely compressible structures just below the skin surface had a colour signal on the Doppler ultrasound suggestive of telangiectatic superficial veins (white arrows). Inside these structures were phleboliths (yellow arrow), appearing as echogenic particles with posterior acoustic shadowing (red arrow). (Color version of figure is available online.)
Fig 3
Fig. 3
Topogram showing left (L) humerus (white arrows), ulna (pink arrows) and radius (yellow arrows) smaller than the opposite side (R). (Color version of figure is available online.)
Fig 4
Fig. 4
Computed tomography showing the diameter of the left humerus (white arrow) smaller than the right (yellow arrow). (Color version of figure is available online.)
Fig 5
Fig. 5
Three-dimensional image demonstrating arteriovenous fistulas on the left back, posterior aspects of arm and hand (3 yellow arrows) with many calcified particles distributed along the left arm, chest, and back. (Color version of figure is available online.)
Fig 6
Fig. 6
The telangiectatic superficial veins (yellow arrows) as seen in the venous phase of computed tomography scan. (Color version of figure is available online.)
See this image and copyright information in PMC

References

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