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Case Reports
. 2021 May 27:66:102433.
doi: 10.1016/j.amsu.2021.102433. eCollection 2021 Jun.

A rare case of congenital cystic adenomatoid malformation: Mimics pneumonia manifestations

Maysaa Badour  1 , Bara'a Hussain  1 , Ali Hammed  2 , Sawssan Ali  1 , Saeed Falyon  1
Affiliations
Case Reports

A rare case of congenital cystic adenomatoid malformation: Mimics pneumonia manifestations

Maysaa Badour et al. Ann Med Surg (Lond). .

Abstract

Introduction and importance: Congenital cystic adenomatoid malformation (CCAM) is a rare malformation, with unknown causes, that affects distal bronchi. It accounts for 25% of congenital pulmonary malformation s and most cases are found in neonates and babies.The mortality rate of prenatally diagnosed cases ranges from 9 to 49%. The risk factors for poor outcome include hydropsfoetalis, microcystic CCAM and the overall size of the lesions.The mainstay of CCAM treatment is surgical excision that prevents complications such as recurrent infections, pneumothorax and malignancy.

Case presentation: Our case is a 4-month-old boy born presented with shortness of breath and poor suckling. He was admitted to intensive care for respiratory distress.

Clinical discussion: A working diagnosis of pneumonia was entertained and the patient given humidified oxygen through nasal prongs, intravenous fluids and antibiotics.Thoracic CT showed a cystic malformation in the left lower lung lobe.Due to continuing recurrent infections and the risk of rupturing of the cyst with subsequent pneumothorax, it was decided to proceed with a left lower lobectomy.The post-operative course was uneventful and the patient was discharged home on the fifth post-operative day.

Conclusion: Congenital cystic adenomatoid malformation should be a differential diagnosis of pneumonia.A real awareness of this rare entity among pediatricians and radiologists should allow early diagnosis and proper treatment.

Keywords: Congenital cystic adenomatoid malformation; Lobectomy; Pneumonia.

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Conflict of interest statement

All authors declared no conflict of interest.

Figures

Fig. 1
Fig. 1
Initial chest x ray shows hyper-lucency of the affected lower left lobe with midline and heart shift to the opposite side and compressive atelectasis of adjacent ipislateral lung lobes.
Fig. 2
Fig. 2
Thoracic CT showed a cystic malformation in the left lower lung lobe. It reveals a large cystic lesion with well defined wall in left lower lung lobe consist of multiple cysts of varying size (3–6 cm).
Fig. 3
Fig. 3
(A-B-C) Intraoperation shows resection of left lower lobe.
Fig. 4
Fig. 4
Follow-up X-ray after 20 days of operation shows normal findings.
See this image and copyright information in PMC

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