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Case Reports
. 2021 Apr 28:13:20-22.
doi: 10.1016/j.jdcr.2021.04.017. eCollection 2021 Jul.

Antimelanoma differentiation-associated gene 5 dermatomyositis associated with acute encephalopathy

Morgan Nguyen  1 , Jacob Groenendyk  2 , Danielle Steker  2 , Parul Kathuria Goyal  2   3 , Cuong V Nguyen  3
Affiliations
Case Reports

Antimelanoma differentiation-associated gene 5 dermatomyositis associated with acute encephalopathy

Morgan Nguyen et al. JAAD Case Rep. .
No abstract available

Keywords: CNS, central nervous system; ILD, interstitial lung disease; MDA5, melanoma differentiation-associated gene 5; connective tissue disease; dermatomyositis; encephalopathy; interstitial lung disease; medical dermatology.

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Conflict of interest statement

None disclosed.

Figures

Fig 1
Fig 1
Cutaneous ulcerations involving the palms of both hands. A, Hands before treatment. B, Hands after 5 weeks of prednisone treatment.
Fig 2
Fig 2
Biopsy of the left second digit. A, Biopsy of palmar surface of the digit demonstrating a pauci-inflammatory process with telangiectasia. B, Focal intraluminal fibrin thrombi are present within the mid reticular dermis. C, A thickened basement membrane zone is noted. D, Increased mucin deposition is present in the superficial dermis and extends into the subcutis. (A and B, Hematoxylin-eosin stain; C, periodic-acid-Schiff-diastase stain; and D, colloidal iron stain; original magnifications: A, ×40; B, ×100; C, ×100; D, ×25.)
See this image and copyright information in PMC

References

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