Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2021 May;21(2):e324-e326.
doi: 10.18295/squmj.2021.21.02.026. Epub 2021 Jun 21.

Cor Triatriatum Sinistrum: A rare disease with a common presentation

Al Rumitha Al Sabri  1 , Niranjan Joshi  1 , Hamood Al Kindi  2 , Khalfan S Al Senaidi  1
Affiliations
Case Reports

Cor Triatriatum Sinistrum: A rare disease with a common presentation

Al Rumitha Al Sabri et al. Sultan Qaboos Univ Med J. 2021 May.

Abstract

Cor triatriatum sinistrum (CTS) is a rare congenital cardiac anomaly characterised by an abnormal septum within the left atrium impairing blood flow to the left ventricle. We report the case of a two-month-old male infant who presented with symptoms of heart failure since the age of two weeks. He was admitted to a local hospital and was managed with antibiotics because of the impression of pneumonia. Due to persistent unresolved tachypnoea and tachycardia, he was referred to Sultan Qaboos University Hospital, Muscat, Oman, in 2019 for cardiac evaluation which confirmed a diagnosis of isolated CTS with severe stenosis and pulmonary hypertension. He underwent an urgent surgical excision of the membrane with uneventful recovery.

Keywords: Case Report; Congenital Heart Disease; Cor Triatriatum Sinistrum; Heart Failure; Oman; Pulmonary Hypertension.

PubMed Disclaimer

Figures

Figure 1
Figure 1
12-leads electrocardiogram of a two-month-old male infant with cor triatriatum sinistrum showing sinus rhythm with right axis deviation and right ventricular hypertrophy with strain pattern.
Figure 2
Figure 2
Chest radiography of a two-month-old male infant with cor triatriatum sinistrum showing features of pulmonary venous congestion and right ventricular hypertrophy.
Figure 3
Figure 3
(A) Four chamber and (B) parasternal long axis echocardiographic views showing the divided left atrium into upper (1) and lower (2) chambers by the membrane (blue arrow). Note the dilated hypertrophied right ventricle and the very small restricted opening in the membrane (red arrow). RA = right atrium; RV = right ventricle; LV = Left ventricle; MV = Mitral valve.
See this image and copyright information in PMC

References

    1. Jha AK, Makhija N. Cor Triatriatum: A review. Semin Cardiothorac Vasc Anesth. 2017;21:178–85. doi: 10.1177/1089253216680495. - DOI - PubMed
    1. Brown J, Hanish SI. Cor triatriatum sinister, atresia of the common pulmonary vein, pulmonary vein stenosis, and cor triatriatum Dexter. In: Mavroudis C, Backer C, editors. Pediatric Cardiac Surgery. Philadelphia, Pennsylvania, USA: Mosby; 2003. pp. 625–33.
    1. Nassar PN, Hamdan RH. Cor triatriatum sinistrum: Classification and imaging modalities. Eur J Cardiovasc Med. 2011;1:84–7. doi: 10.5083/ejcm.20424884.21. - DOI - PMC - PubMed
    1. Humpl T, Reineker K, Manlhiot C, Dipchand AI, Coles JG, McCrindle BW. Cor triatriatum sinistrum in childhood. A single institution’s experience. Can J Cardiol. 2010;26:371–6. doi: 10.1016/s0828-282x(10)70418-9. - DOI - PMC - PubMed
    1. Van Praagh R, Corsini I. Cor triatriatum: Pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and a study of normal development of the pulmonary vein and atrial septum in 83 human embryos. Am Heart J. 1969;78:379–405. doi: 10.1016/0002-8703(69)90046-5. - DOI - PubMed

Publication types

LinkOut - more resources