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Review
. 2021 Sep;162(3):e383-e414.
doi: 10.1016/j.jtcvs.2021.06.019. Epub 2021 Jul 22.

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Hector I Michelena  1 , Alessandro Della Corte  2 , Arturo Evangelista  3 , Joseph J Maleszewski  4 , William D Edwards  4 , Mary J Roman  5 , Richard B Devereux  5 , Borja Fernández  6 , Federico M Asch  7 , Alex J Barker  8 , Lilia M Sierra-Galan  9 , Laurent De Kerchove  10 , Susan M Fernandes  11 , Paul W M Fedak  12 , Evaldas Girdauskas  13 , Victoria Delgado  14 , Suhny Abbara  15 , Emmanuel Lansac  16 , Siddharth K Prakash  17 , Malenka M Bissell  18 , Bogdan A Popescu  19 , Michael D Hope  20 , Marta Sitges  21 , Vinod H Thourani  22 , Phillippe Pibarot  23 , Krishnaswamy Chandrasekaran  24 , Patrizio Lancellotti  25 , Michael A Borger  26 , John K Forrest  27 , John Webb  28 , Dianna M Milewicz  17 , Raj Makkar  29 , Martin B Leon  30 , Stephen P Sanders  31 , Michael Markl  32 , Victor A Ferrari  33 , William C Roberts  34 , Jae-Kwan Song  35 , Philipp Blanke  36 , Charles S White  37 , Samuel Siu  38 , Lars G Svensson  39 , Alan C Braverman  40 , Joseph Bavaria  41 , Thoralf M Sundt  42 , Gebrine El Khoury  10 , Ruggero De Paulis  43 , Maurice Enriquez-Sarano  24 , Jeroen J Bax  14 , Catherine M Otto  44 , Hans-Joachim Schäfers  45
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Free article
Review

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Hector I Michelena et al. J Thorac Cardiovasc Surg. 2021 Sep.
Free article

Abstract

This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.

Keywords: aortopathy; bicuspid aortic valve; classification; nomenclature.

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