[Acquired inhibitory body hemophilia : A life-threatening reason for the tendency of hematoma-genesis]
- PMID: 34338901
- DOI: 10.1007/s10354-021-00866-2
[Acquired inhibitory body hemophilia : A life-threatening reason for the tendency of hematoma-genesis]
Abstract
Here, we report a rare case of acquired hemophilia which was diagnosed months after development of spontaneous hematoma. Clinical symptoms, diagnosis, and treatment are briefly summarized. Acquired hemophilia is a rare potentially life-threatening acquired bleeding disorders which should be considered in patients with acquired spontaneous hematoma.
Es wird über den seltenen Fall einer erworbenen Hemmkörperhämophilie berichtet, die verzögert nach Auftreten einer erworbenen Hämatomneigung diagnostiziert wurde. Klinische Symptomatik, Diagnosestellung und Therapie werden kurz skizziert. Es handelt sich um ein potenziell lebensbedrohliches Krankheitsbild, welches differenzialdiagnostisch bei der Abklärung einer erworbenen Hämatomneigung berücksichtigt werden sollte.
Keywords: Acquired hemophilia; Hematoma; Inhibitors.
© 2021. Springer-Verlag GmbH Austria, ein Teil von Springer Nature.
References
Weiterführende Literatur
-
- Charlebois J, Rivard GÉ, St-Louis J. Management of acquired hemophilia A: review of current evidence. Transfus Apher Sci. 2018;57:717–20. - DOI
-
- Knöbl P. Prevention and management of bleeding episodes in patients with acquired hemophilia A. Drugs. 2018;78:1861–72. - DOI
-
- Kruse-Jarres R, Kempton CL, Baudo F, Collins PW, Knoebl P, Leissinger CA, et al. Acquired hemophilia A: updated review of evidence and treatment guidance. Am J Hematol. 2017;92:695–705. - DOI
-
- Franchini M, Vaglio S, Marano G, Mengoli C, Gentili S, Pupella S, et al. Acquired hemophilia A: a review of recent data and new therapeutic options. Hematology. 2017;22:514–20. - DOI
Publication types
MeSH terms
LinkOut - more resources
Full Text Sources
Medical
