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Case Reports
. 2021 Aug 4:2021:9963564.
doi: 10.1155/2021/9963564. eCollection 2021.

An Interesting Case of Bilateral Facial Palsy due to Granulomatosis with Polyangiitis

Rajish Sanjit Kumar Shil  1 , Jamal Ali Teir  2
Affiliations
Case Reports

An Interesting Case of Bilateral Facial Palsy due to Granulomatosis with Polyangiitis

Rajish Sanjit Kumar Shil et al. Case Rep Rheumatol. .

Abstract

Granulomatosis with polyangiitis (formerly called Wegener's granulomatosis) is a systemic autoimmune disease, which can lead to necrotizing vasculitis affecting small vessels and cause inflammation of blood vessels in the nose, sinuses, throat, lungs, and kidneys. In rare instances, it has shown involvement of the brain and cranial nerves as well. We are reporting a case of granulomatosis with polyangiitis, complicated by bilateral facial palsy due to lower motor neuron involvement of the facial nerve, which has responded well to immunosuppressive treatment, particularly rituximab. It is prudent to be vigilant in investigating patients with atypical presentation for systemic autoimmune diseases, as this approach would affect the patient morbidity and mortality with early initiation of treatment for the disease.

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Conflict of interest statement

The authors declare no conflicts of interest.

Figures

Figure 1
Figure 1
CT thorax showing the cavitary lesion in the right upper lobe of the lung.
Figure 2
Figure 2
CT thorax axial view showing the cavitary lesion in the right upper lobe of the lung.
Figure 3
Figure 3
CT thorax (lung window) axial view showing the cavitary lesion in the right upper lobe of the lung.
Figure 4
Figure 4
MRI brain axial view showing bilateral maxillary sinusitis and left mastoiditis.
See this image and copyright information in PMC

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