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Case Reports
. 2021 Sep 6;9(25):7542-7550.
doi: 10.12998/wjcc.v9.i25.7542.

Neonatal biliary atresia combined with preduodenal portal vein: A case report

Xian-Lan Xiang  1 , Peng Cai  1 , Jun-Gang Zhao  1 , Hao-Wei Zhao  1 , Yu-Liang Jiang  1 , Meng-Lei Zhu  1 , Qi Wang  1 , Rui-Yun Zhang  1 , Zhen-Wei Zhu  1 , Jian-Lei Chen  1 , Zhi-Cheng Gu  1 , Jie Zhu  2
Affiliations
Case Reports

Neonatal biliary atresia combined with preduodenal portal vein: A case report

Xian-Lan Xiang et al. World J Clin Cases. .

Abstract

Background: Congenital biliary atresia is a type of obstruction of the bile ducts inside and outside the liver, which can lead to cholestatic liver cirrhosis and eventually liver failure. The preduodenal portal vein (PD-PV) is a rare developmental malformation of the PV. The PV courses in front of the duodenum. However, very few cases of neonatal biliary atresia combined with PD-PV have been reported in the scientific literature.

Case summary: A 1-mo-and-4-d-old child was admitted to the hospital in January because of yellowish skin. After surgical consultation, surgical intervention was recommended. The child underwent Hilar-jejunal anastomosis, duodenal rhomboid anastomosis, and abdominal drainage under general anesthesia. During the operation, the PV was located at the anterior edge of the duodenum.

Conclusion: Diagnoses: (1) Congenital biliary atresia; (2) PD-PV; and (3) Congenital cardiovascular malformations. Outcomes: Recommendation for liver transplantation. Lessons: The choice of treatment options for neonatal biliary atresia combined with PD-PV.

Keywords: Biliary atresia; Case report; Neonatal; Preduodenal portal vein; Treatment.

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Conflict of interest statement

Conflict-of-interest statement: The authors have no conflicts of interest to disclose.

Figures

Figure 1
Figure 1
The child underwent laparoscopic exploration under general anesthesia. During the operation, the portal vein was located at the anterior edge of the duodenum.
Figure 2
Figure 2
Intraoperative cholangiography showed that the intrahepatic bile duct was visualized by percutaneous puncture catheter-based injection of the contrast agent, but the biliary tract system was not clearly visualized, the duodenum was not visualized, and there was no contrast agent in the abdominal cavity.
See this image and copyright information in PMC

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