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Book

Parry-Romberg Syndrome

Shalin S. Shah  1 , Mohit Chhabra  2
In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan.
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Book

Parry-Romberg Syndrome

Shalin S. Shah et al.
Free Books & Documents

Excerpt

Parry Romberg syndrome (PRS), also referred to as progressive hemifacial atrophy, progressive facial hemiatrophy, or idiopathic hemifacial atrophy, was first described by C Parry and M Romberg. It is an idiopathic, gradually progressive craniofacial asymmetry, following the atrophy of subcutaneous tissue, muscles, osseous, and cartilaginous structures. It manifests in the first 2 decades in morphologically normal-born individuals. It commonly affects 1 or more dermatomes in the trigeminal nerve territory. It has an early onset of ophthalmic and neurological involvement and a variable maxillo-facial or cardiac involvement.

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Conflict of interest statement

Disclosure: Shalin Shah declares no relevant financial relationships with ineligible companies.

Disclosure: Mohit Chhabra declares no relevant financial relationships with ineligible companies.

References

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