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Review
. 2021 Oct 5:9:747812.
doi: 10.3389/fped.2021.747812. eCollection 2021.

Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

Daniel I McLennan  1   2 , Elyan C Ruiz Solano  2   3 , Stephanie S Handler  1   2 , Joy Lincoln  1   2 , Michael E Mitchell  2   3 , Edward C Kirkpatrick  1   2
Affiliations
Review

Pulmonary Vein Stenosis: Moving From Past Pessimism to Future Optimism

Daniel I McLennan et al. Front Pediatr. .

Abstract

Pulmonary Vein Stenosis (PVS) is a rare disease with a prevalence of around 1. 7 cases per 100,000 children under 2 years old. Treatment options for this disease have not provided great results and pathophysiology of this condition is still poorly understood. Here, we will review the history of PVS including diagnostic tools and treatments, the current management approach, and what the future holds for this devastating disease.

Keywords: cardiac catheterization; congenital cardiothoracic surgery; congenital heart disease; pulmonary vein stenosis; pulmonary vein stent angioplasty; sutureless pulmonary vein repair.

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Conflict of interest statement

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest. The Reviewer DI declared a past collaboration with several of the authors DM and SH to the handling editor.

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