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Review
. 2021 Oct 27;18(4):193-197.
doi: 10.1002/cld.1114. eCollection 2021 Oct.

Hepatic Ciliopathy Syndromes

Tamir Diamond  1 , Noor Nema  1 , Jessica Wen  1   2
Affiliations
Review

Hepatic Ciliopathy Syndromes

Tamir Diamond et al. Clin Liver Dis (Hoboken). .

Abstract

Content available: Author Interview and Audio Recording.

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Figures

FIG 1
FIG 1
Hepatic histological features in ARPKD. Low‐magnification (A) and 40× original magnification (B) hematoxylin and eosin stain showing expanded portal tract with fibrosis, multiple dilated irregular bile ducts (arrows), and diminutive portal vein (arrowhead). The lobular architecture remains intact.
FIG 2
FIG 2
Radiological findings in CD. MRCP findings in an 11‐year‐old patient with ARPKD and CD. Diffuse bile duct ectasia involving the intrahepatic and extrahepatic biliary ducts (arrows) with several intrahepatic regions of saccular dilation (asterisks).
See this image and copyright information in PMC

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