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Case Reports
. 2021 Nov 9;14(11):e244578.
doi: 10.1136/bcr-2021-244578.

Primary pulmonary angiosarcoma

Muhammad Kashif Rana  1 , Owais Rahman  2 , Aiden O'Brien  2
Affiliations
Case Reports

Primary pulmonary angiosarcoma

Muhammad Kashif Rana et al. BMJ Case Rep. .

Abstract

Primary pulmonary angiosarcoma is a rare type of malignant vascular tumour with poor prognosis. Diagnosis is often late due to non-specific symptoms and low clinical suspicion for angiosarcoma. A 72-year-old man presented to hospital with a 6-month history of mild progressive dyspnoea, with associated cough, episodes of presyncope and weight loss. CT pulmonary angiogram (CTPA) was reported as a large saddle pulmonary embolism extending into both the right and left pulmonary arteries. Further Multidisciplinary team meeting (MDM) discussion, and review of CTPA and subsequent investigations revealed a large primary pulmonary artery sarcoma which was later confirmed histology. The patient was referred to the cardiothoracic surgeons and underwent left radical pneumonectomy.

Keywords: lung cancer (oncology); pulmonary embolism; respiratory cancer.

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Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
CT pulmonary angiogram. CT PA:Filling defect in main PA and right and left PA. Obstruction of Left PA with no visible contrast.
Figure 2
Figure 2
PET CT. PET CT : FDG avid soft tissue in main PA and Left PA.
Figure 3
Figure 3
(A, B) CT Thorax,10 months postsurgery. CT Thorax: extensive filling defect within right main PA extending down in RLL pulmonary artery and multiple right lung nodule.
See this image and copyright information in PMC

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