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Case Reports
. 2021 Jul 30;7(11):734-738.
doi: 10.1016/j.hrcr.2021.07.010. eCollection 2021 Nov.

Short QT interval as a harbinger of an arrhythmogenic cardiomyopathy

Philippe Chevalier  1   2 , Adrien Moreau  3 , Sylvain Richard  3 , Alexandre Janin  4 , Gilles Millat  4 , Francis Bessière  2 , Antoine Delinière  1   2
Affiliations
Case Reports

Short QT interval as a harbinger of an arrhythmogenic cardiomyopathy

Philippe Chevalier et al. HeartRhythm Case Rep. .
No abstract available

Keywords: Arrhythmogenic cardiomyopathy; Diagnostic; JTc; Repolarization; Short QTc; Sotalol.

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Figures

Figure 1
Figure 1
Electrocardiograms and electrical characteristics. A: Twelve-lead electrocardiograms performed at the time of the initial event (left), 4 years later (middle), and 9 years later (right). B: Short premature ventricular beats that triggered ventricular fibrillation in 1989 and 1993. C: Plot shows how the durations of the corrected QT (ms, black, left axis) and QRS (ms, red, right axis) evolved in the index patient.
Figure 2
Figure 2
SPECT phase analysis imaging. A: Image acquired at the time of ventricular fibrillation occurrence, with no abnormalities. B: Nine years later, with frank right ventricular dilation.
Figure 3
Figure 3
Patient’s heart autopsy. Examples of a microscopic section of the patient’s explanted heart stained with hematoxylin, eosin, and saffron. Inflammation, adipose tissue, and myocardial necrosis are observed.
See this image and copyright information in PMC

References

    1. Basso C., Corrado D., Marcus F.I., Nava A., Thiene G. Arrhythmogenic right ventricular cardiomyopathy. Lancet. 2009;373:1289–1300. - PubMed
    1. Corrado D., Link M.S., Calkins H. Arrhythmogenic right ventricular cardiomyopathy. N Engl J Med. 2017;376:61–72. - PubMed
    1. Cerrone M., Montnach J., Lin X., et al. Plakophilin-2 is required for transcription of genes that control calcium cycling and cardiac rhythm. Nat Commun. 2017;8 - PMC - PubMed
    1. Moreau A., Reisqs J., Delanoe-Ayari H., et al. Deciphering DSC2 arrhythmogenic cardiomyopathy electrical instability: from ion channels to ECG and tailored drug therapy. Clin Transl Med. 2021;11:e319. - PMC - PubMed
    1. Zhang L., Liu L., Kowey P., Fontaine G. The electrocardiographic manifestations of arrhythmogenic right ventricular dysplasia. Curr Cardiol Rev. 2014;10:237–245. - PMC - PubMed

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