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Case Reports
. 2021 Nov 2;13(11):e19207.
doi: 10.7759/cureus.19207. eCollection 2021 Nov.

Idiopathic Intracranial Hypertension in a Malaysian Preschooler

Siti Farhah 'Adilah Basiron  1   2 , Ee Ling Tan  2 , Tun Wang Ch'ng  2 , Othmaliza Othman  1
Affiliations
Case Reports

Idiopathic Intracranial Hypertension in a Malaysian Preschooler

Siti Farhah 'Adilah Basiron et al. Cureus. .

Abstract

A four-year-old girl presented with a three-day history of squint and irritability. Examination showed reduced visual acuity in both eyes, the presence of a false localizing sign, and bilateral optic disc swelling. On investigation, her blood laboratory workup was within the normal range. Imaging of the brain showed no evidence of a space-occupying lesion or cerebral venous sinus thrombosis. The lumbar puncture opening pressure was 27cmH20 and the cerebrospinal fluid workup was normal. The diagnosis of idiopathic intracranial hypertension (IIH) was made based on the diagnostic criteria for pseudotumor cerebri syndrome. She was successfully treated with acetazolamide with resolved symptoms and signs. This highlights the possibility of IIH presenting with inconspicuous symptoms in preschool children, which needs a high index suspicion by clinicians. Hence, solving the challenges in the workup, especially in children, is very crucial.

Keywords: false localizing sign; idiopathic intracranial hypertension (iih); papilledema; pediatric; pseudo tumor cerebri.

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Conflict of interest statement

The authors have declared that no competing interests exist.

Figures

Figure 1
Figure 1. Fundus photo of oculus dexter (OD) shows optic disc swelling at presentation
Figure 2
Figure 2. Fundus photo of oculus sinister (OS) shows optic disc swelling at presentation
Figure 3
Figure 3. Optic disc of oculus dexter (OD) at six weeks follow-up showing improvement of optic disc swelling
Figure 4
Figure 4. Optic disc of oculus sinister (OS) at six weeks follow-up showing improvement of optic disc swelling
See this image and copyright information in PMC

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