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. 2022 May;37(5):1053-1056.
doi: 10.1007/s00467-021-05378-0. Epub 2021 Dec 17.

Non-lupus full-house nephropathy-immune dysregulation as a rare cause of pediatric nephrotic syndrome: Answers

Orsolya Horváth  1   2 , György S Reusz  3 , Veronika Goda  2 , Kata Kelen  1 , István Balogh  4 , Magdolna Kardos  5 , Krisztián Kállay  2 , Áron Cseh  1 , Attila J Szabó  1 , Gergely Kriván  2
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Non-lupus full-house nephropathy-immune dysregulation as a rare cause of pediatric nephrotic syndrome: Answers

Orsolya Horváth et al. Pediatr Nephrol. 2022 May.

Erratum in

No abstract available

Keywords: Autoimmunity; FOXP3 mutation; IPEX syndrome; Primary immunodeficiency (PID); “Full-house” nephropathy (FHN).

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Conflict of interest statement

The authors declare no competing interests.

Figures

Fig. 1
Fig. 1
a Patient flow chart for the Questions part. NS indicates nephrotic syndrome. b Patient flow chart for the Answers part. HSCT indicates hematopoietic stem cell transplantation; IPEX, immunodysregulation, polyendocrinopathy, enteropathy, X-linked (IPEX) syndrome; NS, nephrotic syndrome. Tacrolimus was started as immunosuppressive therapy after the suspicion for IPEX syndrome and continued as graft-versus-host disease prophylaxis for 110 days after HSCT
See this image and copyright information in PMC

References

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