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Observational Study
. 2022 Jan-Feb;33(1):104-107.
doi: 10.1097/SCS.0000000000008022.

Functionality Assessment of Patients With Cleft Hands

Marco Felipe Franco Rosa  1 , Thais Miguel do Monte  1 , Cassio Eduardo Raposo-Amaral  1   2 , Cesar Augusto Raposo-Amaral  1 , Marcos Felipe Marcatto de Abreu  1   3
Affiliations
Observational Study

Functionality Assessment of Patients With Cleft Hands

Marco Felipe Franco Rosa et al. J Craniofac Surg. 2022 Jan-Feb.

Abstract

Background: Ectrodactyly, commonly referred to as cleft hand, is a rare pathology characterized by a deficiency and/or complete absence of the central ray in each hand. In order to customize treatment and improve the patient's quality of life, a more detailed functional evaluation is required. Although several studies evaluate functionality in different types of cleft hands, there are only a few studies that show self-reported evaluations. The objective of this study is to assess the hand function of cleft hand patients.

Methods: An observational retrospective study was performed on 12 cleft hand patients who were treated between 2008 and 2018. There were 8 male patients and 4 female patients. Patients were divided into 2 groups according to their ages: (Group 1) 6 patients between 1 and 7 years of age, and (Group 2) 6 patients between 8 and 18 years of age, respectively. Each group was sub-stratified into 5 subgroups according to the classification system created by Manske and Halikis.

Results: Regardless of age, intragroup hand type comparisons within Groups 1 and 2 did not demonstrate statistically significant differences (P > 0.05) between hand outcomes according to Manske and Halikis classification. Comparison between cleft hand patients and their age matched controls demonstrated statistically significant differences (P < 0.05), as the patients in the control group had higher outcome scores.

Conclusions: Regardless of cleft hand type and patient age, patients with cleft hands experience impaired hand function and present lower outcome scores in comparison to their age matched controls.

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Conflict of interest statement

The authors report no conflicts of interest.

References

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