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. 2022 Mar;49(3):e91-e98.
doi: 10.1111/1346-8138.16301. Epub 2022 Jan 12.

Clinical practice guidelines for pseudoxanthoma elasticum (2017): Clinical Practice Guidelines for Pseudoxanthoma Elasticum Drafting Committee

Akira Iwanaga  1 , Atsushi Utani  1 , Yuta Koike  1 , Yumi Okubo  1 , Yutaka Kuwatsuka  1 , Yuichiro Endo  2 , Hideaki Tanizaki  3 , Mari Wataya-Kaneda  4 , Atsushi Hatamochi  5 , Kosuke Minaga  6 , Tomoo Ogi  7 , Yosuke Yamamoto  8 , Satoshi Ikeda  9 , Eiko Tsuiki  10 , Hiroshi Tamura  11 , Koji Maemura  9 , Takashi Kitaoka  10 , Hiroyuki Murota  1
Affiliations

Clinical practice guidelines for pseudoxanthoma elasticum (2017): Clinical Practice Guidelines for Pseudoxanthoma Elasticum Drafting Committee

Akira Iwanaga et al. J Dermatol. 2022 Mar.

Abstract

Pseudoxanthoma elasticum (PXE) is a progressive hereditary disease that affects tissues such as the skin, retina, blood vessels, and gastrointestinal tracts. Therefore, comprehensive medical care across clinical departments specialized in specific organs is needed to provide the best clinical practices to PXE patients. The Japanese version of clinical guidelines developed by the Japanese Dermatological Association was published in 2017, and aimed to promote equal accessibility of PXE-related medical care. Here, the English version of Japanese guideline is reported, and is intended to be worldwide reference for medical care of PXE.

Keywords: Clinical Practice Guidelines for Pseudoxanthoma Elasticum Drafting Committee; Guideline of the Japanese Dermatological Association; angioid streaks; clinical practice guideline; pseudoxanthoma elasticum.

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References

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