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. 2022 Jul-Aug;33(5):1517-1520.
doi: 10.1097/SCS.0000000000008457. Epub 2022 Jan 12.

Incidence of Non-Syndromic and Syndromic Craniosynostosis in Sweden

Peter Tarnow  1 , Lars Kölby  1 , Giovanni Maltese  1 , Madiha Bhatti Söfteland  1 , Anders Lewén  2 , Pelle Nilsson  2 , Per Enblad  2 , Daniel Nowinski  3
Affiliations

Incidence of Non-Syndromic and Syndromic Craniosynostosis in Sweden

Peter Tarnow et al. J Craniofac Surg. 2022 Jul-Aug.

Abstract

Premature craniosynostosis is a rare condition, with a wide range of incidence estimations in the literature. The aim of this study was to establish the current incidence among the Swedish population. Since the surgical care for these children is centralized to the 2 centers of Sahlgrenska University Hospital and Uppsala University Hospital, the 2 craniofacial hospital registries were examined for surgically treated children, all having a computed tomography verified diagnosis. Results show an incidence of 7.7 cases per 10,000 live births, including 0.60/10,000 syndromic craniosynostosis. Due to information programs among health care staff and a system for early diagnosis through rapid communication, these results seem to mirror the true incidence of craniosynostosis in the Swedish population. The updated incidence data will facilitate healthcare planning and make future studies of possible changes in craniosynostosis incidence more accurate.

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Conflict of interest statement

The authors report no conflicts of interest.

References

    1. Dempsey RF, Monson LA, Maricevich RS, et al. Nonsyndromic craniosynostosis. Clin Plast Surg 2019;46:123–139
    1. Sawh-Martinez R, Steinbacher DM. Syndromic craniosynostosis. Clin Plast Surg 2019;46:141–155
    1. Cohen MM Jr. Craniosynostosis and syndromes with craniosynostosis: incidence, genetics, penetrance, variability, and new syndrome updating. Birth Defects Orig Artic Ser 1979;15:13–63
    1. Shuper A, Merlob P, Grunebaum M, et al. The incidence of isolated craniosynostosis in the newborn infant. Am J Dis Child 1985;139:85–86
    1. Alderman BW, Fernbach SK, Greene C, et al. Diagnostic practice and the estimated prevalence of craniosynostosis in Colorado. Arch Pediatr Adolesc Med 1997;151:159–164

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