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Review
. 2022 Apr;37(2):256-264.
doi: 10.1002/ncp.10842. Epub 2022 Feb 3.

Nutrition management in adults with cystic fibrosis

Jessica M Shape  1 , Marc A Sala  2
Affiliations
Review

Nutrition management in adults with cystic fibrosis

Jessica M Shape et al. Nutr Clin Pract. 2022 Apr.

Abstract

Cystic fibrosis (CF) is a lethal, monogenic, autosomal recessive disease with manifestations in multiple organ systems, including the lungs and gastrointestinal tract, that impact adequate nutrition. This review discusses important aspects of nutrition in adults with CF with a focus on exocrine pancreatic insufficiency, CF-related diabetes, and gastrointestinal motility, as well as how advanced lung disease, CF transmembrane conductance regulator modulators, and aging impact nutrition in CF.

Keywords: CFTR modulator; cystic fibrosis; diabetes mellitus; exocrine pancreatic insufficiency; gastrointestinal motility; lung diseases; nutrition status; nutrition therapy.

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References

REFERENCES

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